Clinical relevance of right ventricular dysplasia/cardiomyopathy.
نویسندگان
چکیده
منابع مشابه
Arrhythmogenic right ventricular dysplasia/ cardiomyopathy versus dilated right ventricular cardiomyopathy: a problematic autopsy diagnosis?
Arrhythmogenic right ventricular dysplasia-cardiomyopathy (ARVD-C) is a rare heart condition with characteristic thinning and fibroadipose tissue replacement of the myocardium of the right ventricular wall. We have seen 20 autopsy cases with morphologic features fitting the criteria of ARVD-C in our hospital in the past 5 years. The clinical characteristics of these patients were not those desc...
متن کاملArrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia
Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is characterized by progressive, fibrofatty replacement of the myocardium, ventricular arrhythmia, sudden death, and progressive heart failure. ARVC/D may be an important cause of syncope, ventricular arrhythmias, electrocardiogram (ECG) abnormalities and/or non-ischemic wall motion abnormalities. Some patients, however, do not ...
متن کاملArrhythmogenic Ventricular Dysplasia/Cardiomyopathy: Insights from the Rationale of Disease Nomenclature and Clinical Perspectives
“Arrhythmogenic right ventricular dysplasia” (ARVD), a heart muscle disorder characterized by the presence of fibro-fatty tissue and ventricular electrical vulnerability related to sudden death, was first described in 1977 by a French team. Since then, other terms such as “arrhythmogenic right ventricular cardiomyopathy” (ARVC), “arrhythmogenic cardiomyopathy” (AC), “left-dominant arrhythmogeni...
متن کاملRight Ventricular Non-Compaction Cardiomyopathy in Children: Brief Review Literature
Right ventricular non-compaction cardiomyopathy (RVNC) is a genetic heterogeneous cardiomyopathy. Despite the increasing number of RVNC cases, the classification and natural history of this disorder are not completely clear. Also, because the pathogenic non-compaction cannot be easily differentiated from normal trabeculations, it is usually hard to accurately measure the prevalence of RV ...
متن کاملClinical and genetic characterization of families with arrhythmogenic right ventricular dysplasia/cardiomyopathy provides novel insights into patterns of disease expression.
BACKGROUND According to clinical-pathological correlation studies, the natural history of arrhythmogenic right ventricular dysplasia/cardiomyopathy is purported to progress from localized to global right ventricular dysfunction, followed by left ventricular (LV) involvement and biventricular pump failure. The inevitable focus on sudden death victims and transplant recipients may, however, have ...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
عنوان ژورنال:
- Heart
دوره 83 1 شماره
صفحات -
تاریخ انتشار 2000